Table 1

Case Summary Illustrating Demographic Data, Diagnosis, and Physiological Variables

Patient #Age (yrs)BSA (m2)DiagnosisTrisomy 21MPAP (mm Hg)TPG (mm Hg)PA Flow (l/min/m2)PVR (WU/m2)Rp/RsQp/Qs
11.80.46AVSD Previous repair, residual VSDYes46275.854.60.242.3
235.21.40AVSDNo1898.601.7 4.0
30.90.41Peri-membranous VSDNo45198.052.30.123.2
442.41.47VSD, ASD Restrictive lung diseaseNo26144.802.90.172.0
50.50.35AVSDYes31216.303.30.193.7
60.80.30VSDNo342110.002.10.142.7
71.10.42AVSDYes43384.408.60.362.0
80.30.32AVSD, oxygen dependencyYes25205.123.90.262.1
90.80.39AVSDYes45332.7212.00.731.3
102.50.52AVSDYes462712.902.10.163.7
110.50.28AVSD, oxygen dependencyYes34226.253.50.213.2
120.30.22VSD Congenital diaphragmatic hernia, oxygen dependencyNo35257.503.30.144.6
130.70.34Residual ascending vein after repair of TAPVCNo24155.702.60.123.0
140.80.30AVSD, large residual VSD after repairYes30163.934.10.321.8
1517.31.33Large patent arterial ductYes52421.6525.40.951.1
1615.91.25Double inlet left ventricle with malposed great arteries; no previous proceduresNo35217.003.00.124.4
171.80.52Peri-membranous VSD Previous coarctation repairNo34136.711.90.122.4
184.00.60Multiple muscular VSDsNo25154.503.30.163.0
190.90.40Peri-membranous VSDNo31189.401.90.143.3
203.90.65AVSD repair Residual primum ASDYes1382.802.90.121.8
211.80.45Peri-membranous VSDNo40249.642.50.143.4
220.30.23AVSD, airway compression, oxygen dependencyNo24124.782.50.112.8
230.40.28Peri-membranous VSD Pulmonary hypertension without heart failureNo33254.895.10.382.1
240.40.30Peri-membranous VSD, oxygen dependencyYes32217.422.80.204.1
252.20.45Peri-membranous VSDNo412410.102.40.133.4
2621.82.08Large multiple VSDsNo62481.5331.41.540.7

ASD = atrial septal defect; AVSD = atrioventricular septal defect; BSA = body surface area; MPAP = mean pulmonary artery pressure; PA = pulmonary artery; PVR = pulmonary vascular resistance; Qp/Qs = left-to-right shunt; Rp/Rs = pulmonary to systemic resistance ratio; TAPVC = total anomalous pulmonary venous connection; TPG = trans-pulmonary gradient; VSD = ventricular septal defect.

  • Right atrial pressure not recorded.